"Ingrained and Defiled-Systemic EBV+ T cell Lymphoma of Childhood"
نویسندگان
چکیده
Systemic EBV+ T cell lymphoma of childhood manifests as a rapidly progressive, life-threatening disorder with fulminant clinical course. Of obscure aetiology, systemic may arise in concurrence primary Epstein Barr viral infection wherein infiltrating lymphocytes demonstrate monoclonal rearrangements within receptor (TCR) genes. delineates virus infected cytotoxic CD8+ or activated CD4+ cells and preponderantly incriminates spleen, hepatic pulmonary parenchyma, lymph nodes, bone marrow diverse cutaneous surfaces
منابع مشابه
systemic ebv t-cell lymphoproliferative disease of young adults.
t/nk cell proliferative ebv associated disease is a rare one which is more common in eastern asian countries. ebv is originally associated with b cells, and ebv associated t cell lymphoma is so rare. hence we decided to describe a patient treated with misleading diagnoses such as tb and sarcoidosis for almost two years. the liver was biopsied after admission in this center, and gastric and colo...
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متن کاملSystemic EBV T-cell lymphoproliferative disease of young adults.
T/NK cell proliferative EBV associated disease is a rare one which is more common in eastern Asian countries. EBV is originally associated with B cells, and EBV associated T cell lymphoma is so rare. Hence we decided to describe a patient treated with misleading diagnoses such as TB and sarcoidosis for almost two years. The liver was biopsied after admission in this center, and gastric and colo...
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The role of Epstein-Barr virus (EBV) in the pathogenesis of severe, chronic active EBV infection and its complications is unclear. We investigated two Japanese patients diagnosed with severe, chronic active EBV infection who subsequently developed EBV-positive T-cell lymphoma. The patients displayed abnormally high antibody titers to EBV antigens, and had evidence of peripheral blood CD4(+) T-c...
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ژورنال
عنوان ژورنال: Biomedical Journal of Scientific and Technical Research
سال: 2023
ISSN: ['2574-1241']
DOI: https://doi.org/10.26717/bjstr.2023.51.008152